The protease SPRTN and SUMOylation coordinate DNA-protein crosslink repair to prevent genome instability

Cell Rep. 2021 Dec 7;37(10):110080. doi: 10.1016/j.celrep.2021.110080.

Abstract

DNA-protein crosslinks (DPCs) are a specific type of DNA lesion in which proteins are covalently attached to DNA. Unrepaired DPCs lead to genomic instability, cancer, neurodegeneration, and accelerated aging. DPC proteolysis was recently identified as a specialized pathway for DPC repair. The DNA-dependent protease SPRTN and the 26S proteasome emerged as two independent proteolytic systems. DPCs are also repaired by homologous recombination (HR), a canonical DNA repair pathway. While studying the cellular response to DPC formation, we identify ubiquitylation and SUMOylation as two major signaling events in DNA replication-coupled DPC repair. DPC ubiquitylation recruits SPRTN to repair sites, promoting DPC removal. DPC SUMOylation prevents DNA double-strand break formation, HR activation, and potentially deleterious genomic rearrangements. In this way, SUMOylation channels DPC repair toward SPRTN proteolysis, which is a safer pathway choice for DPC repair and prevention of genomic instability.

Keywords: BRCA deficiency; DNA replication; DNA-protein crosslink repair; SPRTN protease; SUMO; formaldehyde toxicity; genome stability; homologous recombination; synthetic lethality; ubiquitin.

Publication types

  • Research Support, Non-U.S. Gov't

MeSH terms

  • DNA Breaks, Double-Stranded
  • DNA Damage*
  • DNA Repair*
  • DNA Replication
  • DNA, Neoplasm / biosynthesis
  • DNA, Neoplasm / genetics
  • DNA, Neoplasm / metabolism*
  • DNA-Binding Proteins / genetics
  • DNA-Binding Proteins / metabolism*
  • Female
  • Genomic Instability*
  • HEK293 Cells
  • HeLa Cells
  • Homologous Recombination
  • Humans
  • Male
  • Proteolysis
  • Sumoylation*
  • Synthetic Lethal Mutations

Substances

  • DNA, Neoplasm
  • DNA-Binding Proteins
  • SPRTN protein, human