U.S. flag

An official website of the United States government

Format

Send to:

Choose Destination

Complete deafness

MedGen UID:
108418
•Concept ID:
C0581883
•
Disease or Syndrome
Synonyms: Complete Hearing Loss; Hearing Loss, Complete
SNOMED CT: Complete deafness (8531006)

Definition

Total inability to hear sounds in one or both ears. [from NCI]

Term Hierarchy

CClinical test,  RResearch test,  OOMIM,  GGeneReviews,  VClinVar  
  • CROGVComplete deafness

Professional guidelines

PubMed

Social and health factors associated with adverse treatment outcomes among people with multidrug-resistant tuberculosis in Sierra Leone: a national, retrospective cohort study.
Kamara RF, Saunders MJ, Sahr F, Losa-Garcia JE, Foray L, Davies G, Wingfield T
Lancet Glob Health 2022 Apr;10(4):e543-e554. doi: 10.1016/S2214-109X(22)00004-3. PMID: 35303463Free PMC Article
Clinical characteristics, the diagnostic criteria and management recommendation of otitis media with antineutrophil cytoplasmic antibody (ANCA)-associated vasculitis (OMAAV) proposed by Japan Otological Society.
Harabuchi Y, Kishibe K, Tateyama K, Morita Y, Yoshida N, Okada M, Kunimoto Y, Watanabe T, Inagaki A, Yoshida T, Imaizumi M, Nakamura T, Matsunobu T, Kobayashi S, Iino Y, Murakami S, Takahashi H, Tono T
Auris Nasus Larynx 2021 Feb;48(1):2-14. Epub 2020 Aug 5 doi: 10.1016/j.anl.2020.07.004. PMID: 32768313
Autoimmune sensorineural hearing loss: clinical course and treatment outcome.
Loveman DM, de Comarmond C, Cepero R, Baldwin DM
Semin Arthritis Rheum 2004 Oct;34(2):538-43. doi: 10.1016/j.semarthrit.2003.10.002. PMID: 15505769

Recent clinical studies

Etiology

Analysis of Clinical Prognosis of Totally Deaf Idiopathic Sudden Sensorineural Hearing Loss in Different Ages.
You D, You Q, Liu Y
Altern Ther Health Med 2023 Nov;29(8):506-511. PMID: 37652422
Clinical characteristics, the diagnostic criteria and management recommendation of otitis media with antineutrophil cytoplasmic antibody (ANCA)-associated vasculitis (OMAAV) proposed by Japan Otological Society.
Harabuchi Y, Kishibe K, Tateyama K, Morita Y, Yoshida N, Okada M, Kunimoto Y, Watanabe T, Inagaki A, Yoshida T, Imaizumi M, Nakamura T, Matsunobu T, Kobayashi S, Iino Y, Murakami S, Takahashi H, Tono T
Auris Nasus Larynx 2021 Feb;48(1):2-14. Epub 2020 Aug 5 doi: 10.1016/j.anl.2020.07.004. PMID: 32768313
Behavioral and electrophysiological investigation of hearing and speech outcomes in pre-linguistic deaf children with white matter changes after cochlear implantation.
Shen M, Chen Z, Li Y
Acta Otolaryngol 2019 Dec;139(12):1090-1097. Epub 2019 Oct 31 doi: 10.1080/00016489.2019.1668959. PMID: 31671009
Chemotherapy: present and future.
Terry AR, Plotkin SR
Otolaryngol Clin North Am 2012 Apr;45(2):471-86, x. doi: 10.1016/j.otc.2011.12.013. PMID: 22483828
Cavernous angiomas within the internal auditory canal.
Samii M, Nakamura M, Mirzai S, Vorkapic P, Cervio A
J Neurosurg 2006 Oct;105(4):581-7. doi: 10.3171/jns.2006.105.4.581. PMID: 17044562

Diagnosis

Clinical characteristics, the diagnostic criteria and management recommendation of otitis media with antineutrophil cytoplasmic antibody (ANCA)-associated vasculitis (OMAAV) proposed by Japan Otological Society.
Harabuchi Y, Kishibe K, Tateyama K, Morita Y, Yoshida N, Okada M, Kunimoto Y, Watanabe T, Inagaki A, Yoshida T, Imaizumi M, Nakamura T, Matsunobu T, Kobayashi S, Iino Y, Murakami S, Takahashi H, Tono T
Auris Nasus Larynx 2021 Feb;48(1):2-14. Epub 2020 Aug 5 doi: 10.1016/j.anl.2020.07.004. PMID: 32768313
Early canakinumab therapy for the sensorineural deafness in a family with Muckle-Wells syndrome due to a novel mutation of NLRP3 gene.
Iida Y, Wakiguchi H, Okazaki F, Nakamura T, Yasudo H, Kubo M, Sugahara K, Yamashita H, Suehiro Y, Okayama N, Hashimoto K, Iwamoto N, Kawakami A, Aoki Y, Takada H, Ohga S, Hasegawa S
Clin Rheumatol 2019 Mar;38(3):943-948. Epub 2018 Oct 18 doi: 10.1007/s10067-018-4331-8. PMID: 30338413
Neurosyphilis and classical music: the great composers and "The Great Imitator".
Pedro MKF, Germiniani FMB, Teive HAG
Arq Neuropsiquiatr 2018 Nov;76(11):791-794. doi: 10.1590/0004-282X20180122. PMID: 30570024
Palmoplantar papules and hyperkeratosis in a deaf man.
Taylor SL, Kwatra SG, McMichael AJ
Skinmed 2014 Mar-Apr;12(2):107-9. PMID: 24933850
Cavernous angiomas within the internal auditory canal.
Samii M, Nakamura M, Mirzai S, Vorkapic P, Cervio A
J Neurosurg 2006 Oct;105(4):581-7. doi: 10.3171/jns.2006.105.4.581. PMID: 17044562

Therapy

Clinical characteristics, the diagnostic criteria and management recommendation of otitis media with antineutrophil cytoplasmic antibody (ANCA)-associated vasculitis (OMAAV) proposed by Japan Otological Society.
Harabuchi Y, Kishibe K, Tateyama K, Morita Y, Yoshida N, Okada M, Kunimoto Y, Watanabe T, Inagaki A, Yoshida T, Imaizumi M, Nakamura T, Matsunobu T, Kobayashi S, Iino Y, Murakami S, Takahashi H, Tono T
Auris Nasus Larynx 2021 Feb;48(1):2-14. Epub 2020 Aug 5 doi: 10.1016/j.anl.2020.07.004. PMID: 32768313
Early canakinumab therapy for the sensorineural deafness in a family with Muckle-Wells syndrome due to a novel mutation of NLRP3 gene.
Iida Y, Wakiguchi H, Okazaki F, Nakamura T, Yasudo H, Kubo M, Sugahara K, Yamashita H, Suehiro Y, Okayama N, Hashimoto K, Iwamoto N, Kawakami A, Aoki Y, Takada H, Ohga S, Hasegawa S
Clin Rheumatol 2019 Mar;38(3):943-948. Epub 2018 Oct 18 doi: 10.1007/s10067-018-4331-8. PMID: 30338413
Threshold monitoring of intraoperative auditory steady-state responses for ossiculoplasty surgery.
Liu Q, Feng G, Shang Y, Chi C, Qiao Y, Gao Z
Acta Otolaryngol 2018 Jul;138(7):625-632. Epub 2018 Mar 5 doi: 10.1080/00016489.2018.1436767. PMID: 29504434
Chemotherapy: present and future.
Terry AR, Plotkin SR
Otolaryngol Clin North Am 2012 Apr;45(2):471-86, x. doi: 10.1016/j.otc.2011.12.013. PMID: 22483828
Intravenous azithromycin-induced ototoxicity.
Bizjak ED, Haug MT 3rd, Schilz RJ, Sarodia BD, Dresing JM
Pharmacotherapy 1999 Feb;19(2):245-8. doi: 10.1592/phco.19.3.245.30930. PMID: 10030778

Prognosis

Analysis of Clinical Prognosis of Totally Deaf Idiopathic Sudden Sensorineural Hearing Loss in Different Ages.
You D, You Q, Liu Y
Altern Ther Health Med 2023 Nov;29(8):506-511. PMID: 37652422
Suggested deafness during hypnosis and simulation of hypnosis compared to a distraction and control condition: A study on subjective experience and cortical brain responses.
Franz M, Schmidt B, Hecht H, Naumann E, Miltner WHR
PLoS One 2020;15(10):e0240832. Epub 2020 Oct 29 doi: 10.1371/journal.pone.0240832. PMID: 33119665Free PMC Article
Behavioral and electrophysiological investigation of hearing and speech outcomes in pre-linguistic deaf children with white matter changes after cochlear implantation.
Shen M, Chen Z, Li Y
Acta Otolaryngol 2019 Dec;139(12):1090-1097. Epub 2019 Oct 31 doi: 10.1080/00016489.2019.1668959. PMID: 31671009
Surgical treatment of adult cholesteatoma: long-term follow-up using total reconstruction procedure without staging.
Edfeldt L, Strömbäck K, Kinnefors A, Rask-Andersen H
Acta Otolaryngol 2013 Jan;133(1):28-34. Epub 2012 Oct 31 doi: 10.3109/00016489.2012.707333. PMID: 23113656
Chemotherapy: present and future.
Terry AR, Plotkin SR
Otolaryngol Clin North Am 2012 Apr;45(2):471-86, x. doi: 10.1016/j.otc.2011.12.013. PMID: 22483828

Clinical prediction guides

Analysis of Clinical Prognosis of Totally Deaf Idiopathic Sudden Sensorineural Hearing Loss in Different Ages.
You D, You Q, Liu Y
Altern Ther Health Med 2023 Nov;29(8):506-511. PMID: 37652422
Neuromonitoring of the cochlear nerve during vestibular schwannoma resection and simultaneous cochlear implantation.
Weiss NM, Großmann W, Schraven SP, Oberhoffner T, Mlynski R
HNO 2021 Aug;69(Suppl 2):82-87. Epub 2021 May 21 doi: 10.1007/s00106-021-00997-3. PMID: 34019139
Behavioral and electrophysiological investigation of hearing and speech outcomes in pre-linguistic deaf children with white matter changes after cochlear implantation.
Shen M, Chen Z, Li Y
Acta Otolaryngol 2019 Dec;139(12):1090-1097. Epub 2019 Oct 31 doi: 10.1080/00016489.2019.1668959. PMID: 31671009
Conditional deletion of calcium-modulating cyclophilin ligand causes deafness in mice.
Bryda EC, Johnson NT, Ohlemiller KK, Besch-Williford CL, Moore E, Bram RJ
Mamm Genome 2012 Apr;23(3-4):270-6. Epub 2011 Dec 15 doi: 10.1007/s00335-011-9381-z. PMID: 22170629
Targeted disruption of the Kvlqt1 gene causes deafness and gastric hyperplasia in mice.
Lee MP, Ravenel JD, Hu RJ, Lustig LR, Tomaselli G, Berger RD, Brandenburg SA, Litzi TJ, Bunton TE, Limb C, Francis H, Gorelikow M, Gu H, Washington K, Argani P, Goldenring JR, Coffey RJ, Feinberg AP
J Clin Invest 2000 Dec;106(12):1447-55. doi: 10.1172/JCI10897. PMID: 11120752Free PMC Article

Supplemental Content

Table of contents

    Practice guidelines

    • PubMed
      See practice and clinical guidelines in PubMed. The search results may include broader topics and may not capture all published guidelines. See the FAQ for details.
    • Bookshelf
      See practice and clinical guidelines in NCBI Bookshelf. The search results may include broader topics and may not capture all published guidelines. See the FAQ for details.

    Related information

    • MeSH
      Related Medical Subject Headings
    • PMC Articles
      Related information in PubMed Central Links
    • PubMed
      Related literature resources in PubMed

    Recent activity

    Clear Turn Off Turn On

    Your browsing activity is empty.

    Activity recording is turned off.

    Turn recording back on

    See more...