Figure 1. [Muscle MRI findings in Bethlem muscular dystrophy]. - GeneReviews® - NCBI Bookshelf

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Adam MP, Feldman J, Mirzaa GM, et al., editors. GeneReviews® [Internet]. Seattle (WA): University of Washington, Seattle; 1993-2024.

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Figure 1.

Figure 1.

Muscle MRI findings in Bethlem muscular dystrophy

Axial T₁-weighted images of the upper leg muscles of four individuals with Bethlem muscular dystrophy (a-d). Note the relative sparing of the central part of the vastus lateralis (white arrows) with a rim of increased signal at the periphery of the muscle consistent with an "outside-in" pattern and the prominent increase in signal intensity in the central part of the rectus femoris (black arrowheads) consistent with a "central cloud" pattern (a-d). Both imaging patterns can still be appreciated in the two older individuals of the group, who have evidence of more diffuse involvement (c and d).

Reproduced from Mercuri et al [2005], with permission from Elsevier

From: Collagen VI-Related Dystrophies

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Foley AR, Mohassel P, Donkervoort S, et al. Collagen VI-Related Dystrophies. 2004 Jun 25 [Updated 2021 Mar 11]. In: Adam MP, Feldman J, Mirzaa GM, et al., editors. GeneReviews® [Internet]. Seattle (WA): University of Washington, Seattle; 1993-2024. Figure 1. [Muscle MRI findings in Bethlem muscular dystrophy].
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