Abstract
Intraductal papillary neoplasms of the bile duct (IPNB) are rare precursor lesions of intrahepatic and extrahepatic cholangiocarcinoma that follow an adenoma-carcinoma sequence. According to the histomorphology and the distinct immunohistochemical mucin pattern, four different subtypes are recognized: pancreatobiliary, intestinal, gastric and oncocytic. Differential diagnoses include micropapillary lesions (biliary intraepithelial neoplasms), papillary cystic lesions (intraductal tubulopapillary neoplasms) and cystic lesions (mucinous cystic neoplasms).
MeSH terms
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Bile Duct Neoplasms / classification
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Bile Duct Neoplasms / diagnosis
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Bile Duct Neoplasms / pathology*
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Bile Ducts, Extrahepatic / pathology*
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Bile Ducts, Intrahepatic / pathology*
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Biomarkers, Tumor / analysis
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Carcinoma, Pancreatic Ductal / classification
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Carcinoma, Pancreatic Ductal / diagnosis
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Carcinoma, Pancreatic Ductal / pathology
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Carcinoma, Papillary / classification
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Carcinoma, Papillary / diagnosis
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Carcinoma, Papillary / pathology*
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Cell Transformation, Neoplastic / pathology
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Cholangiocarcinoma / diagnosis
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Cholangiocarcinoma / pathology*
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Diagnosis, Differential
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Female
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Humans
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Liver / pathology
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Male
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Middle Aged
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Mucins / analysis
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Neoplasm Invasiveness
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Neoplasm Staging
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Pancreas / pathology
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Precancerous Conditions / classification
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Precancerous Conditions / diagnosis
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Precancerous Conditions / pathology*
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Prognosis
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Terminology as Topic
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World Health Organization