Detection of six novel mutations in WASP gene in fifteen Iranian Wiskott-Aldrich patients

Iran J Allergy Asthma Immunol. 2012 Dec;11(4):345-8.

Abstract

Wiskott-Aldrich syndrome (WAS) is a life-threatening X-linked recessive immunodeficiency disease described as a clinical triad of thrombocytopenia, eczema, and recurrent infections, caused by mutations of the WAS protein (WASP) gene. The milder form of this disease is X-linked thrombocytopenia (XLT) that presents only as platelet abnormalities. Mutation analysis for 15 boys with Wiskott-Aldrich syndrome was performed. Five previously reported mutations and six novel mutations including G8X, R41X, D283E, P412fsX446, E464X, and AfsX358 were detected.

MeSH terms

  • Case-Control Studies
  • DNA Mutational Analysis / methods
  • Exons
  • Genetic Predisposition to Disease
  • Humans
  • Iran / epidemiology
  • Male
  • Mutation*
  • Polymerase Chain Reaction
  • Wiskott-Aldrich Syndrome / diagnosis
  • Wiskott-Aldrich Syndrome / epidemiology
  • Wiskott-Aldrich Syndrome / genetics*
  • Wiskott-Aldrich Syndrome Protein / genetics*

Substances

  • WAS protein, human
  • Wiskott-Aldrich Syndrome Protein