Introduction: Intraosseous malformations are rarely reported in the maxillofacial area. Because of bone growing processes, it is still a challenge to find the appropriate way to treat this disorder. The gold standard treatment for arteriovenous malformation is an endovascular embolization, combined with surgery.
Methods: The case of a 14-year-old boy with arteriovenous malformation of the mandible was followed during a period of 8 years.
Results: Several embolizations and surgical interventions were required, culminating in bone reconstruction with a fibula graft to achieve normal mandibular form and function. There was no recurrence of the malformation during the follow-up period.
Conclusions: To obtain stable results in the case of intraosseous arteriovenous malformations of the mandible, a combination of embolization and surgery is recommended. Superselective embolization is possible in an emergency case.