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Diabetes Insipidus, Nephrogenic

A genetic or acquired polyuric disorder characterized by persistent hypotonic urine and HYPOKALEMIA. This condition is due to renal tubular insensitivity to VASOPRESSIN and failure to reduce urine volume. It may be the result of mutations of genes encoding VASOPRESSIN RECEPTORS or AQUAPORIN-2; KIDNEY DISEASES; adverse drug effects; or complications from PREGNANCY.

Year introduced: 1995

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Tree Number(s): C12.050.351.968.419.135.500, C12.200.777.419.135.500, C12.950.419.135.500

MeSH Unique ID: D018500

Entry Terms:

  • Nephrogenic Diabetes Insipidus
  • Congenital Nephrogenic Diabetes Insipidus
  • Acquired Nephrogenic Diabetes Insipidus
  • Nephrogenic Diabetes Insipidus, Type I
  • Diabetes Insipidus, Nephrogenic, Type I
  • Diabetes Insipidus, Nephrogenic, X-Linked
  • Diabetes Insipidus, Nephrogenic, Type 1
  • Nephrogenic Diabetes Insipidus, Type II
  • Diabetes Insipidus, Nephrogenic, Autosomal
  • Diabetes Insipidus, Nephrogenic, Type II
  • ADH-Resistant Diabetes Insipidus
  • Diabetes Insipidus Renalis
  • Vasopressin-Resistant Diabetes Insipidus

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