U.S. flag

An official website of the United States government

Format

Send to:

Choose Destination

Abnormality of the intrinsic pathway

MedGen UID:
869188
Concept ID:
C4023610
Anatomical Abnormality
HPO: HP:0010989

Definition

An abnormality of the intrinsic pathway (also known as the contact activation pathway) of the coagulation cascade. [from HPO]

Professional guidelines

PubMed

Vucic S, Stanley Chen KH, Kiernan MC, Hallett M, Benninger DH, Di Lazzaro V, Rossini PM, Benussi A, Berardelli A, Currà A, Krieg SM, Lefaucheur JP, Long Lo Y, Macdonell RA, Massimini M, Rosanova M, Picht T, Stinear CM, Paulus W, Ugawa Y, Ziemann U, Chen R
Clin Neurophysiol 2023 Jun;150:131-175. Epub 2023 Mar 29 doi: 10.1016/j.clinph.2023.03.010. PMID: 37068329Free PMC Article
Neutze D, Roque J
Am Fam Physician 2016 Feb 15;93(4):279-86. PMID: 26926815
Katz BJ, Digre KB
Surv Ophthalmol 2016 Jul-Aug;61(4):466-77. Epub 2016 Feb 12 doi: 10.1016/j.survophthal.2016.02.001. PMID: 26875996

Recent clinical studies

Etiology

Tavassoli N, de Souto Barreto P, Berbon C, Mathieu C, de Kerimel J, Lafont C, Takeda C, Carrie I, Piau A, Jouffrey T, Andrieu S, Nourhashemi F, Beard JR, Soto Martin ME, Vellas B
Lancet Healthy Longev 2022 Jun;3(6):e394-e404. Epub 2022 Jun 9 doi: 10.1016/S2666-7568(22)00097-6. PMID: 36098317
Cenni V, Capanni C, Mattioli E, Schena E, Squarzoni S, Bacalini MG, Garagnani P, Salvioli S, Franceschi C, Lattanzi G
Ageing Res Rev 2020 Sep;62:101073. Epub 2020 May 21 doi: 10.1016/j.arr.2020.101073. PMID: 32446955
Pianou NK, Stavrou PZ, Vlontzou E, Rondogianni P, Exarhos DN, Datseris IE
Hell J Nucl Med 2019 Jan-Apr;22(1):6-9. Epub 2019 Mar 7 doi: 10.1967/s002449910952. PMID: 30843003
Winter WE, Flax SD, Harris NS
Lab Med 2017 Nov 8;48(4):295-313. doi: 10.1093/labmed/lmx050. PMID: 29126301
EFSA GMO Panel Working Group on Animal Feeding Trials
Food Chem Toxicol 2008 Mar;46 Suppl 1:S2-70. Epub 2008 Feb 13 doi: 10.1016/j.fct.2008.02.008. PMID: 18328408

Diagnosis

Vucic S, Stanley Chen KH, Kiernan MC, Hallett M, Benninger DH, Di Lazzaro V, Rossini PM, Benussi A, Berardelli A, Currà A, Krieg SM, Lefaucheur JP, Long Lo Y, Macdonell RA, Massimini M, Rosanova M, Picht T, Stinear CM, Paulus W, Ugawa Y, Ziemann U, Chen R
Clin Neurophysiol 2023 Jun;150:131-175. Epub 2023 Mar 29 doi: 10.1016/j.clinph.2023.03.010. PMID: 37068329Free PMC Article
Bouffard MA
Continuum (Minneap Minn) 2019 Oct;25(5):1194-1214. doi: 10.1212/CON.0000000000000771. PMID: 31584534
Winter WE, Flax SD, Harris NS
Lab Med 2017 Nov 8;48(4):295-313. doi: 10.1093/labmed/lmx050. PMID: 29126301
Dunham-Snary KJ, Wu D, Sykes EA, Thakrar A, Parlow LRG, Mewburn JD, Parlow JL, Archer SL
Chest 2017 Jan;151(1):181-192. Epub 2016 Sep 16 doi: 10.1016/j.chest.2016.09.001. PMID: 27645688Free PMC Article
Katz BJ, Digre KB
Surv Ophthalmol 2016 Jul-Aug;61(4):466-77. Epub 2016 Feb 12 doi: 10.1016/j.survophthal.2016.02.001. PMID: 26875996

Therapy

Nwonu CNS
West Afr J Med 2022 Oct 20;39(10):1075-1983. PMID: 36260866
Oshitari T
Int J Mol Sci 2021 Aug 22;22(16) doi: 10.3390/ijms22169050. PMID: 34445756Free PMC Article
Dubin C, Del Duca E, Guttman-Yassky E
Expert Rev Clin Immunol 2021 Aug;17(8):835-852. Epub 2021 Jul 21 doi: 10.1080/1744666X.2021.1940962. PMID: 34106037
Sawada T, Fujimori D, Yamamoto Y
Immunol Med 2019 Mar;42(1):1-9. Epub 2019 Jun 17 doi: 10.1080/25785826.2019.1628466. PMID: 31204893
EFSA GMO Panel Working Group on Animal Feeding Trials
Food Chem Toxicol 2008 Mar;46 Suppl 1:S2-70. Epub 2008 Feb 13 doi: 10.1016/j.fct.2008.02.008. PMID: 18328408

Prognosis

Fonseca-Montaño MA, Vázquez-Santillán KI, Hidalgo-Miranda A
Front Immunol 2023;14:1194300. Epub 2023 Jun 5 doi: 10.3389/fimmu.2023.1194300. PMID: 37342324Free PMC Article
Sabatino ME, Grondona E, De Paul AL
Front Endocrinol (Lausanne) 2022;13:924942. Epub 2022 Jun 28 doi: 10.3389/fendo.2022.924942. PMID: 35837315Free PMC Article
Peng J, Sun BF, Chen CY, Zhou JY, Chen YS, Chen H, Liu L, Huang D, Jiang J, Cui GS, Yang Y, Wang W, Guo D, Dai M, Guo J, Zhang T, Liao Q, Liu Y, Zhao YL, Han DL, Zhao Y, Yang YG, Wu W
Cell Res 2019 Sep;29(9):725-738. Epub 2019 Jul 4 doi: 10.1038/s41422-019-0195-y. PMID: 31273297Free PMC Article
Behnan J, Finocchiaro G, Hanna G
Brain 2019 Apr 1;142(4):847-866. doi: 10.1093/brain/awz044. PMID: 30946477Free PMC Article
Pianou NK, Stavrou PZ, Vlontzou E, Rondogianni P, Exarhos DN, Datseris IE
Hell J Nucl Med 2019 Jan-Apr;22(1):6-9. Epub 2019 Mar 7 doi: 10.1967/s002449910952. PMID: 30843003

Clinical prediction guides

Sabatino ME, Grondona E, De Paul AL
Front Endocrinol (Lausanne) 2022;13:924942. Epub 2022 Jun 28 doi: 10.3389/fendo.2022.924942. PMID: 35837315Free PMC Article
Peng J, Sun BF, Chen CY, Zhou JY, Chen YS, Chen H, Liu L, Huang D, Jiang J, Cui GS, Yang Y, Wang W, Guo D, Dai M, Guo J, Zhang T, Liao Q, Liu Y, Zhao YL, Han DL, Zhao Y, Yang YG, Wu W
Cell Res 2019 Sep;29(9):725-738. Epub 2019 Jul 4 doi: 10.1038/s41422-019-0195-y. PMID: 31273297Free PMC Article
Pianou NK, Stavrou PZ, Vlontzou E, Rondogianni P, Exarhos DN, Datseris IE
Hell J Nucl Med 2019 Jan-Apr;22(1):6-9. Epub 2019 Mar 7 doi: 10.1967/s002449910952. PMID: 30843003
Thaller DJ, Patrick Lusk C
Biochem Soc Trans 2018 Aug 20;46(4):877-889. Epub 2018 Jul 19 doi: 10.1042/BST20170442. PMID: 30026368Free PMC Article
EFSA GMO Panel Working Group on Animal Feeding Trials
Food Chem Toxicol 2008 Mar;46 Suppl 1:S2-70. Epub 2008 Feb 13 doi: 10.1016/j.fct.2008.02.008. PMID: 18328408

Recent systematic reviews

Menezes Júnior ADS, França-E-Silva ALG, Oliveira JM, Silva DMD
Int J Mol Sci 2023 Dec 30;25(1) doi: 10.3390/ijms25010535. PMID: 38203704Free PMC Article
Liu J, Cao L, Li H, Gao Y, Bu X, Liang K, Bao W, Zhang S, Qiu H, Li X, Hu X, Lu L, Zhang L, Hu X, Huang X, Gong Q
Neurosci Biobehav Rev 2022 Apr;135:104574. Epub 2022 Feb 10 doi: 10.1016/j.neubiorev.2022.104574. PMID: 35151769
Perry BI, McIntosh G, Weich S, Singh S, Rees K
Lancet Psychiatry 2016 Nov;3(11):1049-1058. Epub 2016 Oct 5 doi: 10.1016/S2215-0366(16)30262-0. PMID: 27720402
Sheffield JM, Barch DM
Neurosci Biobehav Rev 2016 Feb;61:108-20. Epub 2015 Dec 14 doi: 10.1016/j.neubiorev.2015.12.007. PMID: 26698018Free PMC Article
Pappa S, Dazzan P
Psychol Med 2009 Jul;39(7):1065-76. Epub 2008 Nov 12 doi: 10.1017/S0033291708004716. PMID: 19000340

Supplemental Content

Table of contents

    Clinical resources

    Practice guidelines

    • PubMed
      See practice and clinical guidelines in PubMed. The search results may include broader topics and may not capture all published guidelines. See the FAQ for details.
    • Bookshelf
      See practice and clinical guidelines in NCBI Bookshelf. The search results may include broader topics and may not capture all published guidelines. See the FAQ for details.

    Consumer resources

    Recent activity

    Your browsing activity is empty.

    Activity recording is turned off.

    Turn recording back on

    See more...